Saudi Journal of Ophthalmology
Volume 24, Issue 3 , Pages 101-104, July 2010

Primary orbital ganglioneuroma in a 2-year-old healthy boy

  • Hattan Al-Khiary, MD

      Affiliations

    • Oculoplastic and Orbit Division, King Khaled Eye Specialist Hospital, Riyadh, Saudi Arabia
    • Corresponding Author InformationCorresponding author. Address: Oculoplastic and Orbit Division, King Khaled Eye Specialist Hospital, P.O. Box 7191, Riyadh 11462, Saudi Arabia. Tel.: +966 1 4821234.
    • ,
  • Ayman Ayoubi, MD

      Affiliations

    • Oculoplastic and Orbit Division, King Khaled Eye Specialist Hospital, Riyadh, Saudi Arabia
    • ,
  • Sahar M. Elkhamary, MD

      Affiliations

    • Diagnostic Radiology Department, King Khaled Eye Specialist Hospital, Riyadh, Saudi Arabia

Received 7 March 2010; received in revised form 16 March 2010; accepted 16 March 2010.

Abstract 

A 2-year-old healthy child presented with progressive unilateral proptosis.

Complete work up including: general examination, detailed ophthalmic evaluation and radiological imaging were done. He underwent orbital exploration via anterior orbitotomy incision and debulking of the tumor was done.

The histopathological examination confirmed the diagnosis of orbital ganglioneuroma.

Ganglioneuroma is an unusual benign tumor of neuroplastic origin with extremely rare orbital involvement with only one prior reported case in a youth. The tumor is slow growing and non-metastasizing. Biopsy is necessary to differentiate it from the malignant neuroblastoma and excision is usually curative.

Keywords: Ganglioneuroma, Neuroblastoma, Unilateral proptosis, Pediatric

 

PII: S1319-4534(10)00046-9

doi:10.1016/j.sjopt.2010.03.003

Saudi Journal of Ophthalmology
Volume 24, Issue 3 , Pages 101-104, July 2010

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